Combined Mobius Syndrome and Tarsal Kink Syndrome- A Unique Presentation.

  • Dr Anuradha Raj Dr. Anuradha Raj, Assistant Professor, Department of Ophthalmology, Himalayan Institute of Medical Sciences, Swami Rama Himalayan University, Swami Ram Nagar, Jolly Grant, Dehradun, Uttarakhand. E-mail: dranuradha_sagar@yahoo.com
  • Prof. R. C. Nagpal Prof. R. C. Nagpal, Professor & Sr. Consultant, Department of Ophthalmology, Himalayan Institute of Medical Sciences, Swami Rama Himalayan University, Swami Ram Nagar, Jolly Grant, Dehradun, Uttarakhand. E-mail : usharamesh8800@yahoo.co.in
  • Prof. Renu Dhasmana Prof. Renu Dhasmana, Professor, Department of Ophthalmology, Himalayan Institute of Medical Sciences, Swami Rama Himalayan University, Swami Ram Nagar, Jolly Grant, Dehradun, Uttarakhand. E-mail : renudhasmana@gmail.com
  • Dr. Amit Maitreya Dr. Amit Maitreya, Assoc. Professor, Department of Ophthalmology, Himalayan Institute of Medical Sciences, Swami Rama Himalayan University, Swami Ram Nagar, Jolly Grant, Dehradun, Uttarakhand. E-mail : drmaitreya@yahoo.com

Abstract

We describe the management of the congenital entropion with tarsal kink in a case of mobius syndrome. Mobius syndrome is extremely rare  congenital neurological disorder results from the underdevelopment of the sixth and seventh cranial nerves which causes  facial paralysis and inability to move the eyes from side to side.  A congenital malformation of the tarsus known as tarsal kink was the associated eyelid anomaly which caused upperlid entropion. A  two year old  girl presented with  both  eyelids entropion of left eye which was corrected by upper lid tarsotomy, marginal rotation and levator  suturing with tarsal plate and lower lid retractors were strengthened by their advancement to the tarsal plate.
Published
Mar 30, 2017
How to Cite
RAJ, Dr Anuradha et al. Combined Mobius Syndrome and Tarsal Kink Syndrome- A Unique Presentation.. Asian Journal of Ophthalmology, [S.l.], v. 15, n. 3, mar. 2017. ISSN 1560-2133. Available at: <http://www.asianjo.com/index.php/AsianJO/article/view/247>. Date accessed: 14 dec. 2017.
Section
Case Report

Keywords

Mobius syndrome, Tarsal kink syndrome, Congenital entropion